id	author	title	date	pages	extension	mime	words	sentences	flesch	summary	cache	txt
cord-016413-lvb79oxo	Efthimiou, Petros	Adult-Onset Still’s Disease	2018-07-14		.txt	text/plain	6126	315	40	Adult-onset Still's disease (AOSD) is a rare systemic, autoinflammatory disorder that often presents in adolescence and early adulthood with fever, rash, and polyarthritis. Mutation of perforin and the MUNC13-4 genes have been seen in patients with macrophage activation syndrome (MAS), a known severe, life-threatening complication of AOSD [3] . Patients who have the chronic articular disease pattern can present with joint erosions making the differential diagnosis from RA problematic, especially in the absence of systemic signs and symptoms. Interleukin-1 receptor antagonist (anakinra) treatment in patients with systemic-onset juvenile idiopathic arthritis or adult onset Still disease: preliminary experience in France Effectiveness of first-line treatment with recombinant interleukin-1 receptor antagonist in steroid-naive patients with new-onset systemic juvenile idiopathic arthritis: results of a prospective cohort study Clinical manifestations of adult-onset Still's disease presenting with erosive arthritis: association with low levels of ferritin and Interleukin-18	./cache/cord-016413-lvb79oxo.txt	./txt/cord-016413-lvb79oxo.txt