id author title date pages extension mime words sentences flesch summary cache txt work_tibafyt4ezemxlzuyiwwnescky B Bourke Byler-like familial cholestasis in an extended kindred 1996.0 6 .pdf application/pdf 5282 929 71 Byler-like familial cholestasis in an extended children from two consanguineous marriages in an Irish kindred is described. acid analysis revealed a non-specific pattern consistent with chronic cholestasis. Keywords: familial cholestasis, Byler disease. disease was clinically and biochemically identical to that of the five living children described the specimens from the older children (patients The pattern of bile acid excretion was consistent with chronic cholestasis rather than an Byler-like familial cholestasis associated with 226 Bourke, Goggin, Walsh, Kennedy, Setchell, Drumm 226 Bourke, Goggin, Walsh, Kennedy, Setchell, Drumm 226 Bourke, Goggin, Walsh, Kennedy, Setchell, Drumm intrahepatic cholestasis and hepatocellular injury consistent with the toxic affect of accumulated bile acids. Progressive familial cholestatic cirrhosis and bile acid metabolism. Progressive familial intrahepatic cholestasis secretion in children with progressive familial intrahepatic Byler-like familial cholestasis in an extended kindred Byler-like familial cholestasis in an extended kindred Byler-like familial cholestasis in an extended kindred ./cache/work_tibafyt4ezemxlzuyiwwnescky.pdf ./txt/work_tibafyt4ezemxlzuyiwwnescky.txt